Year : 2021  |  Volume : 29  |  Issue : 1  |  Page : 62-64

Alveolar Soft Part Sarcoma of the Orbit: A Clinicopathological Report of a Rare Case and Review of the Literature

1 Department of Ophthalmology, University of Maiduguri Teaching Hospital, Maiduguri, Nigeria
2 Department of Human Pathology, University of Maiduguri, Nigeria

Correspondence Address:
Z Y Musa
Department of Ophthalmology, University of Maiduguri Teaching Hospital, Maidugur
Login to access the Email id

Source of Support: None, Conflict of Interest: None

DOI: 10.4103/njo.njo_24_20

Rights and Permissions

Background: Alveolar soft part sarcoma (ASPS) of the orbit is a very rare neoplasm with an uncertain histogenesis. The tumor has an indolent clinical course that requires close and long-term follow-up due to late recurrence and metastasis. Surgery is the primary treatment option with adjunct radiotherapy. Case Report: We present the case of a 25-year-old male who presented with a 5-year history of progressive left eye swelling and loss of vision. He underwent left eye exenteration and histology diagnosed ASPS of the orbit. Conclusion: Orbital ASPS is an uncommon soft tissue tumor. Its prognosis is determined by patient’s age, tumor size, and presence of metastasis at the time of diagnosis. Close and long-term monitoring of the patient is required as recurrence is known to occur up to 10 years after treatment.

Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)

 Article Access Statistics
    PDF Downloaded32    
    Comments [Add]    

Recommend this journal